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A clinico-electroencephalographic study on 14 cases of the early-infantile epileptic
encephalopathy with suppressionburst (EIEE) including long-term follow-up studies
for one year 8 months to 12 years 2 months disclosed the specificity of EIEE in its
developmental aspects. With age, clinical evolution from EIEE to the West syndrome
was observed in as many as 10 cases, among which two cases showed further transition
to the Lennox-Gas taut syndrome. Electroencephalographically, suppression-burst pattern
gradually began to disappear from age of 3 months and disappeared by 6 months in all
the cases, transforming to hypsarhythmia in 10 cases from 2 to 6 months of age, showing
further transition to diffuse slow spike-and-waves in 2 cases at one year and one
month and at 3 years and one month of age, respectively. Changing pattern of EEG were
classifiable into two types which strongly related to the prognosis. These findings
indicated EIEE to be an independent epileptic syndrome as the earliest form of the
age-dependent epileptic encephalopathy.
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References
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© 1987 Published by Elsevier Inc.
