Research Article| Volume 8, ISSUE 6, P590-595, 1986

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Neurophysiological studies in the Leigh syndrome

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      We performed neurophysiological studies in 12 patients with the Leigh syndrome (6 pathologically confirmed and 6 clinically diagnosed). The results are compared with data derived from a literature survey of 173 Leigh syndrome patients. We found no positive contribution of neurophysiological studies towards the diagnosis of the Leigh syndrome.

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      1. Literature references can be requested from the authors.