Abstract
Development and retention of speech is reported in 265 people with Rett syndrome:
30% (80) never gained real words, 55% (145) gained real words and lost them, 15%(40)
retained some words and 6% of the total (16/265) continued to use phrases appropriately.
Morphological studies of the cytoarchitecture of the speech areas in 14 cases indicate
the existence of interhemispheric differences which form part of the infrastructure
for speech processing. Ten adults with Rett syndrome and with meaningful speech are
compared to age matched adults without speech. The profile of mind and strategies
for coping with its problems are described by a family. Although the range in severity
is wide the mental profile is remarkably consistent across the severity range with
regard to both positive and negative aspects.
Keywords
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Article info
Footnotes
☆Rett World Congress, Japan July 2000.
Identification
Copyright
© 2001 Elsevier Science B.V. Published by Elsevier Inc. All rights reserved.
