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West & son: the origins of West syndrome

  • Andrew L. Lux
    Correspondence
    Tel.: +44-177-928-5709
    Affiliations
    Department of Paediatric Neurology, Bristol Royal Hospital for Children, Paul O'Gorman Building, Upper Maudlin Street, Bristol, BS2 8BJ, UK

    Division of Child Health, University of Bristol, Bristol, UK
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      William James West must have felt depressed and frustrated as he penned his letter to the Lancet at the end of January 1841. His son, James Edwin West, had developed a strange nodding of the head at the age of 4 months and had gone on to develop what was obviously a convulsive disorder [
      • West W.J.
      On a peculiar form of infantile convulsions.
      ]. The letter was published on 13th February, James' first birthday.
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