Case report| Volume 23, ISSUE 4, P261-263, July 2001

Download started.


Transient cheiro-oral syndrome due to a ruptured intracranial dermoid cyst


      We present here a case of episodic, pure cheiro-oral syndrome caused by a ruptured intracranial dermoid cyst. Cranial magnetic resonance imaging (MRI) using the fat-suppression method revealed a fatty mass lesion in the subarachnoid space of the left parasellar region and multiple lipid droplets in the subarachnoid space over the left perisylvian area. Although no evidence for it pathogenesis was obtained, the patient's cheiro-oral syndrome could have resulted from a transient vasospasm around the left ventral posterior thalamic nucleus or postcentral gyrus.


      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'


      Subscribe to Brain and Development
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect


        • Lunardi P.
        • Missori P.
        • Rizzo A.
        • Gagliardi F.M.
        Chemical meningitis in ruptured intracranial dermoid. Case report and review of the literature.
        Surg Neurol. 1989; 32: 449-452
        • van der Graaff M.
        • Davies G.
        Status epilepticus due to a ruptured dermoid cyst.
        J Neurol Neurosurg Psychiatry. 1997; 62: 222
        • Sumida M.
        • Taguchi H.
        • Kuroki K.
        A case of recurrent-rupture dermoid cyst (in Japanese).
        No Shinkei Geka (Tokyo). 1999; 27: 261-266
        • Wilms G.
        • Casselman J.
        • Demaerel P.
        • Plets C.
        • De Haene I.
        • Baert A.L.
        CT and MRI of ruptured intracranial dermoids.
        Neuroradiology. 1991; 33: 149-151
        • Smith A.S.
        • Benson J.E.
        • Blaser S.I.
        • Mizushima A.
        • Tarr R.W.
        • Bellon E.M.
        Diagnosis of ruptured intracranial dermoid cyst: value MR over CT.
        Am J Neuroradiol. 1991; 12: 175-180
        • Martin R.
        • Knone A.
        • Schuknecht B.
        • Kuhn W.
        Rapid development of occlusion hydrocephalus by intraventricular fat possibly derived from a ruptured dermoid cyst.
        J Neurol Neurosurg Psychiatry. 1989; 52: 134-135
        • Huang M.H.
        • Chu N.S.
        Pure cheiro-oral syndrome due to a small pontine hematoma: report of a case and review of the literature.
        J Formos Med Assoc. 1994; 93: 636-639
        • Isono O.
        • Kawamura M.
        • Shiota J.
        • Araki S.
        • Hirayama K.
        Cheiro-oral topography of sensory disturbances due to lesions of thalamocortical projections.
        Neurology. 1993; 43: 51-55
        • Aristegui F.J.
        • Delgado R.A.
        • Oleaga Z.L.
        • Hermosa C.C.
        Mollaret's recurrent aseptic meningitis and cerebral epidermoid cyst.
        Pediatr Neurol. 1998; 18: 156-159
        • Laster D.W.
        • Moody D.M.
        • Ball M.R.
        Epidermoid tumors with intraventricular and subarachnoid fat: report of two cases.
        Am J Roentgenol. 1977; 128: 504-507