Research Article| Volume 16, ISSUE 1, P61-64, January 1994

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Infantile bilateral striatal necrosis: chronic and acute manifestations in a single case

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      We report a girl who exhibited a slowly progressive extrapyramidal disorder with onset in early infancy. CT examinations demonstrated progressive atrophy of the cerebrum. At the age of 6 years, acute exacerbation occurred with impairment of consciousness and automomic functions. During the acute episode, CT revealed lesions in the bilateral striatum and globus pallidus.


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