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Abstract
We report a girl who exhibited a slowly progressive extrapyramidal disorder with onset
in early infancy. CT examinations demonstrated progressive atrophy of the cerebrum.
At the age of 6 years, acute exacerbation occurred with impairment of consciousness
and automomic functions. During the acute episode, CT revealed lesions in the bilateral
striatum and globus pallidus.
Keywords
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References
- Developmental neuropathology.in: 1st ed. Springer-Verlag, New York1975: 88-89
- Acute neurological dysfunction associated with destructive lesions of the basal ganglia in children.Ann Neurol. 1982; 12: 328-332
- Infantile bilateral striatal necrosis: clinicopathological classification.Arch Neurol. 1986; 43: 677-680
- Infantile bilateral striatal necrosis: clinical and morphological report of a case and a review of the literature.Acta Neuropathol. 1981; 55: 97-103
- Acute neurologic dysfunction associated with destructive lesions of the basal ganglia: a benign form of infantile bilateral striatal necrosis.J Pediatr. 1990; 117: 578-581
- Neuropathology in glutaric acidemia type 1.Acta Neuropathol. 1986; 76: 590-594
- Bilateral striatal lesions.Dev Med Child Neurol. 1980; 30: 252-257
- Organic acidemias due to defects in lysine oxidation: 2-ketoadipic acidemia and glutaric acidemia.in: 6th ed. The metabolic basis of inherited disease. vol 1. McGraw-Hill, New York1989: 845-853
Article info
Publication history
Accepted:
August 12,
1993
Received:
May 28,
1993
Identification
Copyright
© 1994 Elsevier Science B.V. All rights reserved. Published by Elsevier Inc.