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Abstract
Three types of clinical features at the onset are well known to be characteristic
of acute hemiplegia syndrome (AHS). Type 1 comprises status epilepticus of hemiconvulsions
with fever. Representative diseases of this type are the infectious diseases of the
central nervous system, acute encephalopathy and cerebral vascular diseases. Type
2 comprises status epilepticus of hemiconvulsions without fever. Cerebral vascular
diseases and epilepsy are the major ones of this type. Type 3 comprises hemiplegia
or hemiparesis of sudden onset without fever or convulsions. Most patients with this
type had cerebral vascular diseases, about half of which were moyamoya disease in
Japan. Recent progress in neuroimaging studies has allowed considerable elucidation
of the etiology of AHS. Gadolinium-enhanced MRI showed minimal lesions such as capsular
infarction more clearly than plain MRI. Acetazolamide test99mTc-HMPAO SPECT imaging is one of the useful assisted diagnostic techniques for moyamoya
disease, because it reveals the reserve capacity of the collaterals. [123I]IMP SPECT is useful for the diagnosis and follow-up of acute disseminated encephalomyelitis
(ADEM), as the images of the lesions coincide well with the MRI ones.99mTc-HMPAO SPECT in a case with alternating hemiplegia revealed normoperfusion in the
ictal periods. Four cases of AHS are reported here.
Keywords
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Article info
Publication history
Accepted:
October 5,
1993
Received:
August 7,
1993
Footnotes
This paper was presented as an invited lecture at the 35th annual meeting of the Japanese Society of Child Neurology, Kyoto, 17–19 June 1993.
Identification
Copyright
© 1994 Elsevier Science B.V. All rights reserved. Published by Elsevier Inc.